ICD-10-CM 2027
ICD-10 code for autosomal dominant calpainopathy
From the official ICD-10-CM alphabetic index entry “Calpainopathy (primary) › autosomal dominant”. Page updated September 29, 2026.
About coding autosomal dominant calpainopathy
The ICD-10-CM code for autosomal dominant calpainopathy is G71.031 (Autosomal dominant limb girdle muscular dystrophy).
Within G71.03 (limb girdle muscular dystrophies), G71.031 is specifically for autosomal dominant limb girdle muscular dystrophy. Related codes cover autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction (G71.032), limb girdle muscular dystrophy due to dysferlin dysfunction (G71.033), limb girdle muscular dystrophy due to sarcoglycan dysfunction (G71.034), limb girdle muscular dystrophy due to anoctamin-5 dysfunction (G71.035), limb girdle muscular dystrophy due to fukutin related protein dysfunction (G71.036), other limb girdle muscular dystrophy (G71.038) and limb girdle muscular dystrophy, unspecified (G71.039).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about autosomal dominant calpainopathy ICD-10 codes
What is the ICD-10 code for autosomal dominant calpainopathy?
- G71.031 — Autosomal dominant limb girdle muscular dystrophy.
Is G71.031 billable?
- Yes. G71.031 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.031 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.031 as a principal diagnosis.
Is G71.031 a CC or MCC?
- No. G71.031 is neither a CC nor an MCC under MS-DRG v44.0.