ICD-10-CM 2027
ICD-10 code for Babington's disease
From the official ICD-10-CM alphabetic index entry “Babington's disease (familial hemorrhagic telangiectasia)”. Page updated September 29, 2026.
About coding Babington's disease
The ICD-10-CM code for Babington's disease is I78.0 (Hereditary hemorrhagic telangiectasia).
Within I78 (diseases of capillaries), I78.0 is specifically for hereditary hemorrhagic telangiectasia. Related codes cover nevus, non-neoplastic (I78.1), other diseases of capillaries (I78.8) and disease of capillaries, unspecified (I78.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 299 (Peripheral Vascular Disorders with MCC, relative weight 1.5842), DRG 300 (Peripheral Vascular Disorders with CC, relative weight 1.0464) and DRG 301 (Peripheral Vascular Disorders without CC/MCC, relative weight 0.7133), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Babington's disease ICD-10 codes
What is the ICD-10 code for Babington's disease?
- I78.0 — Hereditary hemorrhagic telangiectasia.
Is I78.0 billable?
- Yes. I78.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I78.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I78.0 as a principal diagnosis.
Is I78.0 a CC or MCC?
- No. I78.0 is neither a CC nor an MCC under MS-DRG v44.0.