ICD-10-CM 2027 diagnosis code
I78.0Hereditary hemorrhagic telangiectasia
I78.0 is a valid, billable ICD-10-CM code for hereditary hemorrhagic telangiectasia. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Looking up by condition? See ICD-10 code for Babington's disease, ICD-10 code for Osler-Rendu disease, ICD-10 code for Weber-Osler syndrome, ICD-10 code for Rendu-Osler-Weber disease or syndrome.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About I78.0
I78.0 is the ICD-10-CM diagnosis code for hereditary hemorrhagic telangiectasia. It belongs to category I78 (diseases of capillaries), block I70-I79 (diseases of arteries, arterioles and capillaries) and chapter 9 (diseases of the circulatory system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within I78 (diseases of capillaries), I78.0 is specifically for hereditary hemorrhagic telangiectasia. Related codes cover nevus, non-neoplastic (I78.1), other diseases of capillaries (I78.8) and disease of capillaries, unspecified (I78.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 299 (Peripheral Vascular Disorders with MCC, relative weight 1.5842), DRG 300 (Peripheral Vascular Disorders with CC, relative weight 1.0464) and DRG 301 (Peripheral Vascular Disorders without CC/MCC, relative weight 0.7133), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 448.0 (hereditary hemorrhagic telangiectasia).
Coding notes
- Rendu-Osler-Weber disease
Notes that apply from higher levels
Instructions written at a parent level also apply to I78.0.
Broader instructions also apply from Chapter 9: Diseases of the circulatory system.
Alphabetic index entries
18 entriesTerms in the official ICD-10-CM index that lead to I78.0.
- Angioma › hemorrhagicum hereditaria
- Angiomatosis › hemorrhagic familial
- Angiomatosis › hereditary familial
- Babington's disease (familial hemorrhagic telangiectasia)
- Disease, diseased › Babington's (familial hemorrhagic telangiectasia)
- Disease, diseased › Goldstein's (familial hemorrhagic telangiectasia)
- Disease, diseased › Osler-Rendu (familial hemorrhagic telangiectasia)
- Disease, diseased › Rendu-Osler-Weber (familial hemorrhagic telangiectasia)
- Epistaxis (multiple) › hereditary
- Goldstein's disease (familial hemorrhagic telangiectasia)
- Osler (-Weber)-Rendu disease
- Rendu-Osler-Weber disease or syndrome
- Syndrome › Osler-Weber-Rendu
- Syndrome › Rendu-Osler-Weber
- Telangiectasia, telangiectasis (verrucous) › familial
- Telangiectasia, telangiectasis (verrucous) › hemorrhagic, hereditary (congenital) (senile)
- Telangiectasia, telangiectasis (verrucous) › hereditary, hemorrhagic (congenital) (senile)
- Weber-Osler syndrome
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 05 · Diseases and Disorders of the Circulatory System
ICD-9-CM equivalent
Converter →- 448.0Hereditary hemorrhagic telangiectasiaexact
From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about I78.0
Is I78.0 billable?
- Yes. I78.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I78.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I78.0 as a principal diagnosis.
Is I78.0 a CC or MCC?
- No. I78.0 is neither a CC nor an MCC under MS-DRG v44.0.
What DRG does I78.0 group to?
- I78.0 is used in the MS-DRG v44.0 logic for MS-DRG 299 (Peripheral Vascular Disorders with MCC), MS-DRG 300 (Peripheral Vascular Disorders with CC) and MS-DRG 301 (Peripheral Vascular Disorders without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for I78.0?
- The CMS General Equivalence Mappings map I78.0 to ICD-9-CM 448.0.