ICD-10-CM 2027
ICD-10 code for beta sarcoglycanopathy
From the official ICD-10-CM alphabetic index entry “Sarcoglycanopathy › beta”. Page updated September 29, 2026.
About coding beta sarcoglycanopathy
The ICD-10-CM code for beta sarcoglycanopathy is G71.0342 (Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction).
Within G71.034 (limb girdle muscular dystrophy due to sarcoglycan dysfunction), G71.0342 is specifically for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. Related codes cover unspecified (G71.0340), alpha sarcoglycan dysfunction (G71.0341) and other sarcoglycan dysfunction (G71.0349).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about beta sarcoglycanopathy ICD-10 codes
What is the ICD-10 code for beta sarcoglycanopathy?
- G71.0342 — Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction.
Is G71.0342 billable?
- Yes. G71.0342 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.0342 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.0342 as a principal diagnosis.
Is G71.0342 a CC or MCC?
- No. G71.0342 is neither a CC nor an MCC under MS-DRG v44.0.