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ICD-10-CM 2027 diagnosis code

G71.0342Limb girdle muscular dystrophy due to beta sarcoglycan dysfunction

✓ Billable / specific

G71.0342 is a valid, billable ICD-10-CM code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.Short description: Limb girdle musc dyst due to beta sarcoglycan dysfunction

Code last changed in FY2023 (effective October 1, 2022). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About G71.0342

G71.0342 is the ICD-10-CM diagnosis code for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. It belongs to category G71 (primary disorders of muscles), block G70-G73 (diseases of myoneural junction and muscle) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within G71.034 (limb girdle muscular dystrophy due to sarcoglycan dysfunction), G71.0342 is specifically for limb girdle muscular dystrophy due to beta sarcoglycan dysfunction. Related codes cover unspecified (G71.0340), alpha sarcoglycan dysfunction (G71.0341) and other sarcoglycan dysfunction (G71.0349).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It was added in FY2023, effective October 1, 2022.

Coding notes

Applicable toConditions and synonyms classified to this code
  • Beta sarcoglycanopathy
  • Limb girdle muscular dystrophy due to beta-sarcoglycan deficiency
  • Limb girdle muscular dystrophy type 2E

Notes that apply from higher levels

Instructions written at a parent level also apply to G71.0342.

› From G71 Primary disorders of muscles
Excludes2
  • arthrogryposis multiplex congenita (Q74.3)
  • metabolic disorders (E70-E88)
  • myositis (M60.-)

Broader instructions also apply from Chapter 6: Diseases of the nervous system.

Alphabetic index entries

5 entries

Terms in the official ICD-10-CM index that lead to G71.0342.

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2023 (effective 10/1/2022): Added
  • No changes since FY2023.

Common questions about G71.0342

Is G71.0342 billable?

Yes. G71.0342 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can G71.0342 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict G71.0342 as a principal diagnosis.

Is G71.0342 a CC or MCC?

No. G71.0342 is neither a CC nor an MCC under MS-DRG v44.0.

What DRG does G71.0342 group to?

G71.0342 is used in the MS-DRG v44.0 logic for MS-DRG 091 (Other Disorders of Nervous System with MCC), MS-DRG 092 (Other Disorders of Nervous System with CC) and MS-DRG 093 (Other Disorders of Nervous System without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.