ICD-10-CM 2027
ICD-10 code for Calpainopathy
Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction
From the official ICD-10-CM alphabetic index entry “Calpainopathy (primary)”. Page updated September 29, 2026.
About coding Calpainopathy
The ICD-10-CM code for Calpainopathy is G71.032 (Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on G71.032.
Within G71.03 (limb girdle muscular dystrophies), G71.032 is specifically for autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction. Related codes cover autosomal dominant limb girdle muscular dystrophy (G71.031), limb girdle muscular dystrophy due to dysferlin dysfunction (G71.033), limb girdle muscular dystrophy due to sarcoglycan dysfunction (G71.034), limb girdle muscular dystrophy due to anoctamin-5 dysfunction (G71.035), limb girdle muscular dystrophy due to fukutin related protein dysfunction (G71.036), other limb girdle muscular dystrophy (G71.038) and limb girdle muscular dystrophy, unspecified (G71.039).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific Calpainopathy codes (official index)
Common questions about Calpainopathy ICD-10 codes
What is the ICD-10 code for Calpainopathy?
- G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction. More specific codes apply when the documentation supports them: G71.031, G71.032.
What is the ICD-10 code for autosomal dominant calpainopathy?
- G71.031 — Autosomal dominant limb girdle muscular dystrophy.
What is the ICD-10 code for autosomal recessive calpainopathy?
- G71.032 — Autosomal recessive limb girdle muscular dystrophy due to calpain-3 dysfunction.
Is G71.032 billable?
- Yes. G71.032 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.032 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.032 as a principal diagnosis.
Is G71.032 a CC or MCC?
- No. G71.032 is neither a CC nor an MCC under MS-DRG v44.0.