ICD-10-CM 2027
ICD-10 code for Cantrell's syndrome
Other specified congenital malformation syndromes, not elsewhere classified
From the official ICD-10-CM alphabetic index entry “Cantrell's syndrome”. Page updated September 29, 2026.
About coding Cantrell's syndrome
The ICD-10-CM code for Cantrell's syndrome is Q87.89 (Other specified congenital malformation syndromes, not elsewhere classified).
Within Q87.8, choose Q87.89 (Other specified congenital malformation syndromes, not elsewhere classified) only when documentation doesn't support a more specific option: Alport syndrome (Q87.81), arterial tortuosity syndrome (Q87.82), Bardet-Biedl syndrome (Q87.83), Laurence-Moon syndrome (Q87.84), MED13L syndrome (Q87.85), Kleefstra syndrome (Q87.86), Hao-Fountain Syndrome (Q87.87) and CTNNB1 syndrome (Q87.88).
Use an additional code(s) to identify all associated manifestations.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Cantrell's syndrome ICD-10 codes
What is the ICD-10 code for Cantrell's syndrome?
- Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified.
Is Q87.89 billable?
- Yes. Q87.89 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q87.89 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q87.89 as a principal diagnosis.
Is Q87.89 a CC or MCC?
- Q87.89 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.