Q87.8Other specified congenital malformation syndromes, not elsewhere classified

Q87.8 is the ICD-10-CM diagnosis code for other specified congenital malformation syndromes, not elsewhere classified. It belongs to category Q87 (other specified congenital malformation syndromes affecting multiple systems), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is a header code, so it can't be reported by itself; one of its 9 subcodes must be used instead.

Within Q87, choose Q87.8 (Other specified congenital malformation syndromes, not elsewhere classified) only when documentation doesn't support a more specific option: congenital malformation syndromes predominantly affecting facial appearance (Q87.0), congenital malformation syndromes predominantly associated with short stature (Q87.1), congenital malformation syndromes predominantly involving limbs (Q87.2), congenital malformation syndromes involving early overgrowth (Q87.3), Marfan syndrome (Q87.4), other congenital malformation syndromes with other skeletal changes (Q87.5) and Loeys-Dietz syndrome (Q87.A).

To report this condition, pick the subcode that matches the documentation: Q87.81 (syndrome), Q87.82 (syndrome), Q87.83 (syndrome), Q87.84 (syndrome), Q87.85 (syndrome), Q87.86 (syndrome), Q87.87 (syndrome), Q87.88 (syndrome) and 1 more.

Don't report Q87.8 together with the conditions in its Excludes1 note: Zellweger syndrome (E71.510).

Use an additional code(s) to identify all associated manifestations.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.