ICD-10-CM 2027
ICD-10 code for cardiomyopathy
From the official ICD-10-CM alphabetic index entry “Cardiomyopathy (familial) (idiopathic)”. Page updated September 29, 2026.
About coding cardiomyopathy
The ICD-10-CM code for cardiomyopathy is I42.9 (Cardiomyopathy, unspecified). The official index lists 53 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on I42.9.
Within I42, choose I42.9 (unspecified) only when documentation doesn't support a more specific option: dilated cardiomyopathy (I42.0), obstructive hypertrophic cardiomyopathy (I42.1), other hypertrophic cardiomyopathy (I42.2), Endomyocardial (eosinophilic) disease (I42.3), endocardial fibroelastosis (I42.4), other restrictive cardiomyopathy (I42.5), alcoholic cardiomyopathy (I42.6), due to drug and external agent (I42.7) and 1 more.
Code first: pre-existing cardiomyopathy complicating pregnancy and puerperium (O99.4).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
More specific cardiomyopathy codes (official index)
- alcoholic I42.6 — Alcoholic cardiomyopathy
- amyloid E85.4 — Organ-limited amyloidosis
- transthyretin-related (ATTR) familial E85.4 — Organ-limited amyloidosis
- arrhythmogenic I42.81 — Arrhythmogenic cardiomyopathy
- biventricular I42.81 — Arrhythmogenic cardiomyopathy
- ventricular (left) (right) I42.81 — Arrhythmogenic cardiomyopathy
- arteriosclerotic
- beriberi E51.12 — Wet beriberi
- cobalt-beer I42.6 — Alcoholic cardiomyopathy
- congenital I42.4 — Endocardial fibroelastosis
- congestive I42.00 — Dilated cardiomyopathy, unspecified
- constrictive NOS I42.5 — Other restrictive cardiomyopathy
- dilated I42.00 — Dilated cardiomyopathy, unspecified
- familial-genetic I42.01 — Familial-genetic dilated cardiomyopathy
- specified (nonfamilial) NEC I42.09 — Other dilated cardiomyopathy
- due to
- alcohol I42.6 — Alcoholic cardiomyopathy
- beriberi E51.12 — Wet beriberi
- cardiac glycogenosis E74.02 — Pompe disease
- drugs I42.7 — Cardiomyopathy due to drug and external agent
- external agents NEC I42.7 — Cardiomyopathy due to drug and external agent
- Friedreich's ataxia G11.11 — Friedreich ataxia
- myotonia atrophica G71.11 — Myotonic muscular dystrophy
- progressive muscular dystrophy G71.09 — Other specified muscular dystrophies
- glycogen storage E74.02 — Pompe disease
- hypertensive
- hypertrophic (nonobstructive) I42.2 — Other hypertrophic cardiomyopathy
- obstructive I42.1 — Obstructive hypertrophic cardiomyopathy
- congenital Q24.8 — Other specified congenital malformations of heart
- in
- Chagas' disease (chronic) B57.2 — Chagas' disease (chronic) with heart involvement
- acute B57.0 — Acute Chagas' disease with heart involvement
- sarcoidosis D86.85 — Sarcoid myocarditis
- ischemic I25.5 — Ischemic cardiomyopathy
- metabolic E88.9 — Metabolic disorder, unspecified
- thyrotoxic E05.90 — Thyrotoxicosis, unspecified without thyrotoxic crisis or storm
- with thyroid storm E05.91 — Thyrotoxicosis, unspecified with thyrotoxic crisis or storm
- newborn I42.89 — Other cardiomyopathies not elsewhere classified
- congenital I42.4 — Endocardial fibroelastosis
- non-ischemic I42.89 — Other cardiomyopathies not elsewhere classified
- nutritional E63.9 — Nutritional deficiency, unspecified
- beriberi E51.12 — Wet beriberi
- obscure of Africa I42.89 — Other cardiomyopathies not elsewhere classified
- peripartum O90.3 — Peripartum cardiomyopathy
- postpartum O90.3 — Peripartum cardiomyopathy
- restrictive NEC I42.5 — Other restrictive cardiomyopathy
- rheumatic I09.0 — Rheumatic myocarditis
- secondary I42.9 — Cardiomyopathy, unspecified
- specified NEC I42.89 — Other cardiomyopathies not elsewhere classified
- stress induced I51.81 — Takotsubo syndrome
- takotsubo I51.81 — Takotsubo syndrome
- thyrotoxic E05.90 — Thyrotoxicosis, unspecified without thyrotoxic crisis or storm
- with thyroid storm E05.91 — Thyrotoxicosis, unspecified with thyrotoxic crisis or storm
- toxic NEC I42.7 — Cardiomyopathy due to drug and external agent
- transthyretin-related (ATTR) familial amyloid E85.4 — Organ-limited amyloidosis
- tuberculous A18.84 — Tuberculosis of heart
- viral B33.24 — Viral cardiomyopathy
Common questions about cardiomyopathy ICD-10 codes
What is the ICD-10 code for cardiomyopathy?
- I42.9 — Cardiomyopathy, unspecified. More specific codes apply when the documentation supports them: I42.6, E85.4, E85.4, I42.81 and others below.
What is the ICD-10 code for alcoholic cardiomyopathy?
- I42.6 — Alcoholic cardiomyopathy.
What is the ICD-10 code for amyloid cardiomyopathy?
- E85.4 — Organ-limited amyloidosis.
What is the ICD-10 code for arrhythmogenic cardiomyopathy?
- I42.81 — Arrhythmogenic cardiomyopathy.
What is the ICD-10 code for beriberi cardiomyopathy?
- E51.12 — Wet beriberi.
What is the ICD-10 code for cobalt-beer cardiomyopathy?
- I42.6 — Alcoholic cardiomyopathy.
What is the ICD-10 code for congenital cardiomyopathy?
- I42.4 — Endocardial fibroelastosis.
Is I42.9 billable?
- Yes. I42.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can I42.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict I42.9 as a principal diagnosis.
Is I42.9 a CC or MCC?
- I42.9 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.