ICD-10-CM 2027 diagnosis code
G11.11Friedreich ataxia
G11.11 is a valid, billable ICD-10-CM code for friedreich ataxia. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.
Code last changed in FY2021 (effective October 1, 2020). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About G11.11
G11.11 is the ICD-10-CM diagnosis code for Friedreich ataxia. It belongs to category G11 (hereditary ataxia), block G10-G14 (systemic atrophies primarily affecting the central nervous system) and chapter 6 (diseases of the nervous system). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within G11.1 (early-onset cerebellar ataxia), G11.11 is specifically for Friedreich ataxia. Related codes cover unspecified (G11.10) and other early-onset cerebellar ataxia (G11.19).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC, relative weight 1.8438), DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC, relative weight 1.2002) and DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC, relative weight 0.9247), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It was added in FY2021, effective October 1, 2020.
Coding notes
- Autosomal recessive Friedreich ataxia
- Friedreich ataxia with retained reflexes
Notes that apply from higher levels
Instructions written at a parent level also apply to G11.11.
› From G11 Hereditary ataxia
Broader instructions also apply from Chapter 6: Diseases of the nervous system.
Alphabetic index entries
13 entriesTerms in the official ICD-10-CM index that lead to G11.11.
- Ataxia, ataxy, ataxic › autosomal recessive Friedreich
- Ataxia, ataxy, ataxic › Friedreich's (heredofamilial) (cerebellar) (spinal) (with retained reflexes)
- Ataxia, ataxy, ataxic › hereditary › spinal (Friedreich's)
- Ataxia, ataxy, ataxic › spinal › hereditary (Friedreich's)
- Cardiomyopathy (familial) (idiopathic) › due to › Friedreich's ataxia
- Disease, diseased › Friedreich's › combined systemic or ataxia
- Friedreich's › ataxia
- Friedreich's › combined systemic disease
- Friedreich's › sclerosis (cerebellum) (spinal cord)
- Myocardiopathy (congestive) (constrictive) (familial) (hypertrophic nonobstructive) (idiopathic) (infiltrative) (obstructive) (primary) (restrictive) (sporadic) › in (due to) › Friedreich's ataxia
- Sclerosis, sclerotic › Friedreich's (spinal cord)
- Sclerosis, sclerotic › hereditary › spinal (Friedreich's ataxia)
- Sclerosis, sclerotic › spinal (cord) (progressive) › hereditary (Friedreich's) (mixed form)
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 01 · Diseases and Disorders of the Nervous System
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2021 (effective 10/1/2020): Added
- No changes since FY2021.
Common questions about G11.11
Is G11.11 billable?
- Yes. G11.11 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G11.11 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G11.11 as a principal diagnosis.
Is G11.11 a CC or MCC?
- G11.11 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.
What DRG does G11.11 group to?
- G11.11 is used in the MS-DRG v44.0 logic for MS-DRG 058 (Multiple Sclerosis and Cerebellar Ataxia with MCC), MS-DRG 059 (Multiple Sclerosis and Cerebellar Ataxia with CC) and MS-DRG 060 (Multiple Sclerosis and Cerebellar Ataxia without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.