ICD-10-CM 2027
ICD-10 code for carnitine deficiency muscle
Muscle carnitine palmitoyltransferase deficiency
From the official ICD-10-CM alphabetic index entry “Muscle, muscular › carnitine (palmityltransferase) deficiency”. Page updated September 29, 2026.
About coding carnitine deficiency muscle
The ICD-10-CM code for carnitine deficiency muscle is E71.314 (Muscle carnitine palmitoyltransferase deficiency).
Within E71.31 (disorders of fatty-acid oxidation), E71.314 is specifically for muscle carnitine palmitoyltransferase deficiency. Related codes cover long chain/very long chain acyl CoA dehydrogenase deficiency (E71.310), Medium chain acyl CoA dehydrogenase deficiency (E71.311), short chain acyl CoA dehydrogenase deficiency (E71.312), Glutaric aciduria type II (E71.313) and other disorders of fatty-acid oxidation (E71.318).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about carnitine deficiency muscle ICD-10 codes
What is the ICD-10 code for carnitine deficiency muscle?
- E71.314 — Muscle carnitine palmitoyltransferase deficiency.
Is E71.314 billable?
- Yes. E71.314 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.314 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.314 as a principal diagnosis.
Is E71.314 a CC or MCC?
- E71.314 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.