ICD-10-CM 2027 diagnosis code
E71.31Disorders of fatty-acid oxidation
E71.31 is a header code, so it can't be reported by itself. Choose one of the 6 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About E71.31
E71.31 is the ICD-10-CM diagnosis code for disorders of fatty-acid oxidation. It belongs to category E71 (disorders of branched-chain amino-acid metabolism and fatty-acid metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 6 subcodes must be used instead.
Within E71.3 (disorders of fatty-acid metabolism), E71.31 is specifically for disorders of fatty-acid oxidation. Related codes cover disorder of fatty-acid metabolism, unspecified (E71.30), disorders of ketone metabolism (E71.32) and other disorders of fatty-acid metabolism (E71.39).
To report this condition, pick the subcode that matches the documentation: E71.310 (deficiency), E71.311 (deficiency), E71.312 (deficiency), E71.313 (II), E71.314 (deficiency) and E71.318 (oxidation).
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under E71.31
- E71.310Long chain/very long chain acyl CoA dehydrogenase deficiencyBillable
- E71.311Medium chain acyl CoA dehydrogenase deficiencyBillable
- E71.312Short chain acyl CoA dehydrogenase deficiencyBillable
- E71.313Glutaric aciduria type IIBillable
- E71.314Muscle carnitine palmitoyltransferase deficiencyBillable
- E71.318Other disorders of fatty-acid oxidationBillable
Notes that apply from higher levels
Instructions written at a parent level also apply to E71.31.
Broader instructions also apply from E70-E88 Metabolic disorders and Chapter 4: Endocrine, nutritional and metabolic diseases.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about E71.31
Is E71.31 billable?
- No. E71.31 is a header code. Report one of its more specific subcodes instead.