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ICD-10-CM 2027

ICD-10 code for congenital

Choose a code from the options below based on the documentation.

From the official ICD-10-CM alphabetic index entry “Congenital”. Page updated September 29, 2026.

About coding congenital

The official ICD-10-CM index doesn't give a single default code for congenital; the code depends on the details below.

More specific congenital codes (official index)

  • aortic septum Q25.49 — Other congenital malformations of aorta
  • intrinsic factor deficiency D51.0 — Vitamin B12 deficiency anemia due to intrinsic factor deficiency
  • malformation

Common questions about congenital ICD-10 codes

What is the ICD-10 code for aortic septum congenital?

Q25.49 — Other congenital malformations of aorta.

What is the ICD-10 code for intrinsic factor deficiency congenital?

D51.0 — Vitamin B12 deficiency anemia due to intrinsic factor deficiency.