ICD-10-CM 2027
ICD-10 code for congenital bronchiectasis
From the official ICD-10-CM alphabetic index entry “Bronchiectasis (cylindrical) (diffuse) (fusiform) (localized) (saccular) › congenital”. Page updated September 29, 2026.
About coding congenital bronchiectasis
The ICD-10-CM code for congenital bronchiectasis is Q33.4 (Congenital bronchiectasis).
Within Q33 (congenital malformations of lung), Q33.4 is specifically for congenital bronchiectasis. Related codes cover congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 190 (Chronic Obstructive Pulmonary Disease with MCC, relative weight 1.0748), DRG 191 (Chronic Obstructive Pulmonary Disease with CC, relative weight 0.8261) and DRG 192 (Chronic Obstructive Pulmonary Disease without CC/MCC, relative weight 0.6288), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about congenital bronchiectasis ICD-10 codes
What is the ICD-10 code for congenital bronchiectasis?
- Q33.4 — Congenital bronchiectasis.
Is Q33.4 billable?
- Yes. Q33.4 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q33.4 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q33.4 as a principal diagnosis.
Is Q33.4 a CC or MCC?
- Q33.4 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.