ICD-10-CM 2027
ICD-10 code for congenital myxedema
From the official ICD-10-CM alphabetic index entry “Myxedema (adult) (idiocy) (infantile) (juvenile) › congenital”. Page updated September 29, 2026.
About coding congenital myxedema
The ICD-10-CM code for congenital myxedema is E00.1 (Congenital iodine-deficiency syndrome, myxedematous type).
Within E00 (congenital iodine-deficiency syndrome), E00.1 is specifically for congenital iodine-deficiency syndrome, myxedematous type. Related codes cover neurological type (E00.0), mixed type (E00.2) and unspecified (E00.9).
Use an additional code (F70-F79) to identify associated intellectual disabilities.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about congenital myxedema ICD-10 codes
What is the ICD-10 code for congenital myxedema?
- E00.1 — Congenital iodine-deficiency syndrome, myxedematous type.
Is E00.1 billable?
- Yes. E00.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E00.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E00.1 as a principal diagnosis.
Is E00.1 a CC or MCC?
- No. E00.1 is neither a CC nor an MCC under MS-DRG v44.0.