ICD-10-CM 2027
ICD-10 code for congenital poikiloderma
From the official ICD-10-CM alphabetic index entry “Poikiloderma › congenital”. Page updated September 29, 2026.
About coding congenital poikiloderma
The ICD-10-CM code for congenital poikiloderma is Q82.8 (Other specified congenital malformations of skin).
Within Q82, choose Q82.8 (Other specified congenital malformations of skin) only when documentation doesn't support a more specific option: hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6) and congenital malformation of skin, unspecified (Q82.9).
Don't report Q82.8 together with the conditions in its Excludes1 note: Ehlers-Danlos syndromes (Q79.6-).
The conditions in its Excludes2 note aren't part of Q82.8, but may be coded alongside it if the patient has both: disorders of pyrophosphate metabolism (E83.82-).
Don't confuse with (Excludes1 for Q82.8)
- Ehlers-Danlos syndromes (Q79.6-)
Common questions about congenital poikiloderma ICD-10 codes
What is the ICD-10 code for congenital poikiloderma?
- Q82.8 — Other specified congenital malformations of skin.
Is Q82.8 billable?
- Yes. Q82.8 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.8 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.8 as a principal diagnosis.
Is Q82.8 a CC or MCC?
- No. Q82.8 is neither a CC nor an MCC under MS-DRG v44.0.