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ICD-10-CM 2027 diagnosis code

Q82.2Congenital cutaneous mastocytosis

✓ Billable / specificPOA exempt

Q82.2 is a valid, billable ICD-10-CM code for congenital cutaneous mastocytosis. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.

Code last changed in FY2018 (effective October 1, 2017). Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data

About Q82.2

Q82.2 is the ICD-10-CM diagnosis code for congenital cutaneous mastocytosis. It belongs to category Q82 (other congenital malformations of skin), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q82 (other congenital malformations of skin), Q82.2 is specifically for congenital cutaneous mastocytosis. Related codes cover hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6), other specified congenital malformations of skin (Q82.8) and congenital malformation of skin, unspecified (Q82.9).

Don't report Q82.2 together with the conditions in its Excludes1 note: cutaneous mastocytosis NOS (D47.01), diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01), malignant mastocytosis (C96.2-), systemic mastocytosis (D47.02) and 1 more.

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728), DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772) and DRG 795 (Normal Newborn, relative weight 0.2022), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2018 (title revised).

Before ICD-10, this condition was coded in ICD-9-CM as 757.33 (congenital pigmentary anomalies of skin).

Coding notes

Applicable toConditions and synonyms classified to this code
  • Congenital diffuse cutaneous mastocytosis
  • Congenital maculopapular cutaneous mastocytosis
  • Congenital urticaria pigmentosa
Excludes1Not coded here — never report together with this code
  • cutaneous mastocytosis NOS (D47.01)
  • diffuse cutaneous mastocytosis (with onset after newborn period) (D47.01)
  • malignant mastocytosis (C96.2-)
  • systemic mastocytosis (D47.02)
  • urticaria pigmentosa (non-congenital) (with onset after newborn period) (D47.01)

Notes that apply from higher levels

Instructions written at a parent level also apply to Q82.2.

› From Q82 Other congenital malformations of skin
Excludes1
  • acrodermatitis enteropathica (E83.2)
  • congenital erythropoietic porphyria (E80.0)
  • pilonidal cyst or sinus (L05.-)
  • Sturge-Weber (-Dimitri) syndrome (Q85.89)

Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

Alphabetic index entries

6 entries

Terms in the official ICD-10-CM index that lead to Q82.2.

Codes whose notes reference Q82.2

MS-DRG v44.0 grouping

All DRGs →

Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.

MDC 09 · Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast

MDC 15 · Newborns and Other Neonates with Conditions Originating in the Perinatal Period

ICD-9-CM equivalent

Converter →
  • 757.33Congenital pigmentary anomalies of skinapproximate

From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.

Code history

  1. 2016
  2. 2017
  3. 2018
  4. 2019
  5. 2020
  6. 2021
  7. 2022
  8. 2023
  9. 2024
  10. 2025
  11. 2026
  12. 2027
  • FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
  • FY2018 (effective 10/1/2017): Title revised — was “Mastocytosis”

Common questions about Q82.2

Is Q82.2 billable?

Yes. Q82.2 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can Q82.2 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict Q82.2 as a principal diagnosis.

Is Q82.2 a CC or MCC?

No. Q82.2 is neither a CC nor an MCC under MS-DRG v44.0.

What DRG does Q82.2 group to?

Q82.2 is used in the MS-DRG v44.0 logic for MS-DRG 606 (Minor Skin Disorders with MCC), MS-DRG 607 (Minor Skin Disorders without MCC) and MS-DRG 795 (Normal Newborn). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.

What is the ICD-9 code for Q82.2?

The CMS General Equivalence Mappings map Q82.2 to ICD-9-CM 757.33.