ICD-10-CM 2027
ICD-10 code for congenital syndrome
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Syndrome › congenital”. Page updated September 29, 2026.
About coding congenital syndrome
The official ICD-10-CM index doesn't give a single default code for congenital syndrome; the code depends on the details below.
More specific congenital syndrome codes (official index)
- affecting multiple systems NEC Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
- central alveolar hypoventilation G47.35 — Congenital central alveolar hypoventilation syndrome
- facial diplegia Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- muscular hypertrophy-cerebral Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified
- oculo-auriculovertebral Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- oculofacial diplegia (Moebius) Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance
- rubella (manifest) P35.0 — Congenital rubella syndrome
Common questions about congenital syndrome ICD-10 codes
What is the ICD-10 code for central alveolar hypoventilation congenital syndrome?
- G47.35 — Congenital central alveolar hypoventilation syndrome.
What is the ICD-10 code for facial diplegia congenital syndrome?
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance.
What is the ICD-10 code for muscular hypertrophy-cerebral congenital syndrome?
- Q87.89 — Other specified congenital malformation syndromes, not elsewhere classified.
What is the ICD-10 code for oculo-auriculovertebral congenital syndrome?
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance.
What is the ICD-10 code for oculofacial diplegia congenital syndrome?
- Q87.0 — Congenital malformation syndromes predominantly affecting facial appearance.
What is the ICD-10 code for rubella congenital syndrome?
- P35.0 — Congenital rubella syndrome.