ICD-10-CM 2027 diagnosis code
Q87.0Congenital malformation syndromes predominantly affecting facial appearance
Q87.0 is a valid, billable ICD-10-CM code for congenital malformation syndromes predominantly affecting facial appearance. It can be reported on claims for dates of service from October 1, 2026 – September 30, 2027.Short description: Congen malform syndromes predom affecting facial appearance
Looking up by condition? See ICD-10 code for Cyclopia, ICD-10 code for Cyclopism, ICD-10 code for Robin syndrome, ICD-10 code for Whistling face.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About Q87.0
Q87.0 is the ICD-10-CM diagnosis code for congenital malformation syndromes predominantly affecting facial appearance. It belongs to category Q87 (other specified congenital malformation syndromes affecting multiple systems), block Q80-Q89 (other congenital malformations) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.
Within Q87 (other specified congenital malformation syndromes affecting multiple systems), Q87.0 is specifically for congenital malformation syndromes predominantly affecting facial appearance. Related codes cover congenital malformation syndromes predominantly associated with short stature (Q87.1), congenital malformation syndromes predominantly involving limbs (Q87.2), congenital malformation syndromes involving early overgrowth (Q87.3), Marfan syndrome (Q87.4), other congenital malformation syndromes with other skeletal changes (Q87.5), other specified congenital malformation syndromes, not elsewhere classified (Q87.8) and Loeys-Dietz syndrome (Q87.A).
Use an additional code(s) to identify all associated manifestations.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Before ICD-10, this condition was coded in ICD-9-CM as 755.55 (Acrocephalosyndactyly) and 756.0 (anomalies of skull and face bones).
Coding notes
- Acrocephalopolysyndactyly
- Acrocephalosyndactyly [Apert]
- Cryptophthalmos syndrome
- Cyclopia
- Goldenhar syndrome
- Moebius syndrome
- Oro-facial-digital syndrome
- Robin syndrome
- Whistling face
Notes that apply from higher levels
Instructions written at a parent level also apply to Q87.0.
› From Q87 Other specified congenital malformation syndromes affecting multiple systems
- code(s) to identify all associated manifestations
Broader instructions also apply from Chapter 17: Congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.
Alphabetic index entries
39 entriesTerms in the official ICD-10-CM index that lead to Q87.0.
- Acrocephalopolysyndactyly
- Acrocephalosyndactyly
- Aglossia-adactylia syndrome
- Apert's syndrome
- Carpenter's syndrome
- Cryptophthalmos › syndrome
- Cyclopia, cyclops
- Cyclopism
- Dyscranio-pygo-phalangy
- Dysplasia › oculodentodigital
- Fraser's syndrome
- Freeman Sheldon syndrome
- Goldenhar (-Gorlin) syndrome
- Gorlin-Chaudry-Moss syndrome
- Hallerman-Streiff syndrome
- Hanhart's syndrome
- Marchesani (-Weill) syndrome
- Meyer-Schwickerath and Weyers syndrome
- Moebius, Möbius › syndrome
- Moebius, Möbius › syndrome › congenital oculofacial paralysis (with other anomalies)
- Mohr's syndrome (Types I and II)
- Papillon-Léage and Psaume syndrome
- Paralysis, paralytic (complete) (incomplete) › oculofacial, congenital (Moebius)
- Pierre Robin deformity or syndrome
- Robin (-Pierre) syndrome
- Syndrome › congenital › facial diplegia
- Syndrome › congenital › oculo-auriculovertebral
- Syndrome › congenital › oculofacial diplegia (Moebius)
- Syndrome › cryptophthalmos
- Syndrome › eyelid-malar-mandible
- Syndrome › first arch
- Syndrome › micrognathia-glossoptosis
- Syndrome › oral-facial-digital
- Syndrome › oro-facial-digital
- Syndrome › oto-palatal-digital
- Syndrome › whistling face
- Tower skull › with exophthalmos
- Ullrich-Feichtiger syndrome
- Whistling face
Codes whose notes reference Q87.0
MS-DRG v44.0 grouping
All DRGs →Inpatient MS-DRGs this diagnosis can group to, as the principal or a secondary diagnosis, depending on the rest of the claim.
MDC 08 · Diseases and Disorders of the Musculoskeletal System and Connective Tissue
ICD-9-CM equivalent
Converter →From the CMS 2018 General Equivalence Mappings (GEMs), the final GEMs release.
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about Q87.0
Is Q87.0 billable?
- Yes. Q87.0 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q87.0 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q87.0 as a principal diagnosis.
Is Q87.0 a CC or MCC?
- No. Q87.0 is neither a CC nor an MCC under MS-DRG v44.0.
What DRG does Q87.0 group to?
- Q87.0 is used in the MS-DRG v44.0 logic for MS-DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC), MS-DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC) and MS-DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC). Which one applies depends on whether it is the principal diagnosis and on the rest of the claim.
What is the ICD-9 code for Q87.0?
- The CMS General Equivalence Mappings map Q87.0 to ICD-9-CM 755.55 and 756.0.