ICD-10-CM 2027
ICD-10 code for congenital syphilis
From the official ICD-10-CM alphabetic index entry “Syphilis, syphilitic (acquired) › congenital”. Page updated September 29, 2026.
About coding congenital syphilis
The ICD-10-CM code for congenital syphilis is A50.9 (Congenital syphilis, unspecified). The official index lists 34 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on A50.9.
Within A50, choose A50.9 (unspecified) only when documentation doesn't support a more specific option: early congenital syphilis, symptomatic (A50.0), early congenital syphilis, latent (A50.1), early congenital syphilis, unspecified (A50.2), late congenital syphilitic oculopathy (A50.3), late congenital neurosyphilis [juvenile neurosyphilis] (A50.4), other late congenital syphilis, symptomatic (A50.5), late congenital syphilis, latent (A50.6) and late congenital syphilis, unspecified (A50.7).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 867 (Other Infectious and Parasitic Diseases Diagnoses with MCC, relative weight 2.1859), DRG 868 (Other Infectious and Parasitic Diseases Diagnoses with CC, relative weight 1.0235) and DRG 869 (Other Infectious and Parasitic Diseases Diagnoses without CC/MCC, relative weight 0.6787), in MDC 18 (Infectious and Parasitic Diseases, Systemic or Unspecified Sites), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific congenital syphilis codes (official index)
- with
- paresis (general) A50.45 — Juvenile general paresis
- tabes (dorsalis) A50.45 — Juvenile general paresis
- taboparesis A50.45 — Juvenile general paresis
- chorioretinitis, choroiditis A50.01 — Early congenital syphilitic oculopathy
- early, or less than 2 years after birth NEC A50.2 — Early congenital syphilis, unspecified
- with manifestations
- latent (without manifestations) A50.1 — Early congenital syphilis, latent
- negative spinal fluid test A50.1 — Early congenital syphilis, latent
- serology positive A50.1 — Early congenital syphilis, latent
- symptomatic A50.09 — Other early congenital syphilis, symptomatic
- cutaneous A50.06 — Early cutaneous congenital syphilis
- mucocutaneous A50.07 — Early mucocutaneous congenital syphilis
- oculopathy A50.01 — Early congenital syphilitic oculopathy
- osteochondropathy A50.02 — Early congenital syphilitic osteochondropathy
- pharyngitis A50.03 — Early congenital syphilitic pharyngitis
- pneumonia A50.04 — Early congenital syphilitic pneumonia
- rhinitis A50.05 — Early congenital syphilitic rhinitis
- visceral A50.08 — Early visceral congenital syphilis
- interstitial keratitis A50.31 — Late congenital syphilitic interstitial keratitis
- juvenile neurosyphilis A50.45 — Juvenile general paresis
- late, or 2 years or more after birth NEC A50.7 — Late congenital syphilis, unspecified
- chorioretinitis, choroiditis A50.32 — Late congenital syphilitic chorioretinitis
- interstitial keratitis A50.31 — Late congenital syphilitic interstitial keratitis
- juvenile neurosyphilis A50.45 — Juvenile general paresis
- latent (without manifestations) A50.6 — Late congenital syphilis, latent
- negative spinal fluid test A50.6 — Late congenital syphilis, latent
- serology positive A50.6 — Late congenital syphilis, latent
- symptomatic or with manifestations NEC A50.59 — Other late congenital syphilis, symptomatic
- arthropathy A50.55 — Late congenital syphilitic arthropathy
- cardiovascular A50.54 — Late congenital cardiovascular syphilis
- Clutton's joints A50.51 — Clutton's joints
- Hutchinson's teeth A50.52 — Hutchinson's teeth
- Hutchinson's triad A50.53 — Hutchinson's triad
- osteochondropathy A50.56 — Late congenital syphilitic osteochondropathy
- saddle nose A50.57 — Syphilitic saddle nose
Common questions about congenital syphilis ICD-10 codes
What is the ICD-10 code for congenital syphilis?
- A50.9 — Congenital syphilis, unspecified. More specific codes apply when the documentation supports them: A50.45, A50.45, A50.45, A50.01 and others below.
What is the ICD-10 code for interstitial keratitis congenital syphilis?
- A50.31 — Late congenital syphilitic interstitial keratitis.
What is the ICD-10 code for juvenile neurosyphilis congenital syphilis?
- A50.45 — Juvenile general paresis.
Is A50.9 billable?
- Yes. A50.9 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can A50.9 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict A50.9 as a principal diagnosis.
Is A50.9 a CC or MCC?
- No. A50.9 is neither a CC nor an MCC under MS-DRG v44.0.