ICD-10-CM 2027 diagnosis code
A50.4Late congenital neurosyphilis [juvenile neurosyphilis]
A50.4 is a header code, so it can't be reported by itself. Choose one of the 7 more specific codes beneath it.
Code unchanged since ICD-10-CM took effect on October 1, 2015. Source: official FY2027 ICD-10-CM release from CDC/NCHS and CMS. Page updated September 29, 2026. About our data
About A50.4
A50.4 is the ICD-10-CM diagnosis code for late congenital neurosyphilis [juvenile neurosyphilis]. It belongs to category A50 (congenital syphilis), block A50-A64 (infections with a predominantly sexual mode of transmission) and chapter 1 (certain infectious and parasitic diseases). It is a header code, so it can't be reported by itself; one of its 7 subcodes must be used instead.
Within A50 (congenital syphilis), A50.4 is specifically for late congenital neurosyphilis [juvenile neurosyphilis]. Related codes cover early congenital syphilis, symptomatic (A50.0), early congenital syphilis, latent (A50.1), early congenital syphilis, unspecified (A50.2), late congenital syphilitic oculopathy (A50.3), other late congenital syphilis, symptomatic (A50.5), late congenital syphilis, latent (A50.6), late congenital syphilis, unspecified (A50.7) and unspecified (A50.9).
To report this condition, pick the subcode that matches the documentation: A50.40 (unspecified), A50.41 (meningitis), A50.42 (encephalitis), A50.43 (polyneuropathy), A50.44 (atrophy), A50.45 (paresis) and A50.49 (neurosyphilis).
Don't report A50.4 together with the conditions in its Excludes1 note: Hutchinson's triad (A50.53).
Use an additional code to identify any associated mental disorder.
It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.
Specific codes under A50.4
- A50.40Late congenital neurosyphilis, unspecifiedBillable
- A50.41Late congenital syphilitic meningitisBillable
- A50.42Late congenital syphilitic encephalitisBillable
- A50.43Late congenital syphilitic polyneuropathyBillable
- A50.44Late congenital syphilitic optic nerve atrophyBillable
- A50.45Juvenile general paresisBillable
- A50.49Other late congenital neurosyphilisBillable
Coding notes
- Hutchinson's triad (A50.53)
- code to identify any associated mental disorder
Notes that apply from higher levels
Instructions written at a parent level also apply to A50.4.
Broader instructions also apply from A50-A64 Infections with a predominantly sexual mode of transmission and Chapter 1: Certain infectious and parasitic diseases.
Codes whose notes reference A50.4
- G91.4Code first
Code history
- 2016
- 2017
- 2018
- 2019
- 2020
- 2021
- 2022
- 2023
- 2024
- 2025
- 2026
- 2027
- FY2016 (effective 10/1/2015): Added (first year of ICD-10-CM)
- No changes since FY2016.
Common questions about A50.4
Is A50.4 billable?
- No. A50.4 is a header code. Report one of its more specific subcodes instead.