ICD-10-CM 2027
ICD-10 code for Coproporphyria
From the official ICD-10-CM alphabetic index entry “Coproporphyria, hereditary”. Page updated September 29, 2026.
About coding Coproporphyria
The ICD-10-CM code for Coproporphyria is E80.29 (Other porphyria).
Within E80.2, choose E80.29 (Other porphyria) only when documentation doesn't support a more specific option: unspecified porphyria (E80.20) and acute intermittent (hepatic) porphyria (E80.21).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Coproporphyria ICD-10 codes
What is the ICD-10 code for Coproporphyria?
- E80.29 — Other porphyria.
Is E80.29 billable?
- Yes. E80.29 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E80.29 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E80.29 as a principal diagnosis.
Is E80.29 a CC or MCC?
- E80.29 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.