E80.2Other and unspecified porphyria

E80.2 is the ICD-10-CM diagnosis code for other and unspecified porphyria. It belongs to category E80 (disorders of porphyrin and bilirubin metabolism), block E70-E88 (metabolic disorders) and chapter 4 (endocrine, nutritional and metabolic diseases). It is a header code, so it can't be reported by itself; one of its 3 subcodes must be used instead.

Within E80, choose E80.2 (Other and unspecified porphyria) only when documentation doesn't support a more specific option: hereditary erythropoietic porphyria (E80.0), porphyria cutanea tarda (E80.1), defects of catalase and peroxidase (E80.3), Gilbert syndrome (E80.4), Crigler-Najjar syndrome (E80.5), other disorders of bilirubin metabolism (E80.6) and disorder of bilirubin metabolism, unspecified (E80.7).

To report this condition, pick the subcode that matches the documentation: E80.20 (porphyria), E80.21 (porphyria) and E80.29 (porphyria).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.