ICD-10-CM 2027
ICD-10 code for Darier disease
From the official ICD-10-CM alphabetic index entry “Darier (-White) disease (congenital)”. Page updated September 29, 2026.
About coding Darier disease
The ICD-10-CM code for Darier disease is Q82.8 (Other specified congenital malformations of skin). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q82.8.
Within Q82, choose Q82.8 (Other specified congenital malformations of skin) only when documentation doesn't support a more specific option: hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6) and congenital malformation of skin, unspecified (Q82.9).
Don't report Q82.8 together with the conditions in its Excludes1 note: Ehlers-Danlos syndromes (Q79.6-).
The conditions in its Excludes2 note aren't part of Q82.8, but may be coded alongside it if the patient has both: disorders of pyrophosphate metabolism (E83.82-).
More specific Darier disease codes (official index)
- meaning erythema annulare centrifugum L53.1 — Erythema annulare centrifugum
Don't confuse with (Excludes1 for Q82.8)
- Ehlers-Danlos syndromes (Q79.6-)
Common questions about Darier disease ICD-10 codes
What is the ICD-10 code for Darier disease?
- Q82.8 — Other specified congenital malformations of skin. More specific codes apply when the documentation supports them: L53.1.
What is the ICD-10 code for meaning erythema annulare centrifugum darier disease?
- L53.1 — Erythema annulare centrifugum.
Is Q82.8 billable?
- Yes. Q82.8 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.8 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.8 as a principal diagnosis.
Is Q82.8 a CC or MCC?
- No. Q82.8 is neither a CC nor an MCC under MS-DRG v44.0.