ICD-10-CM 2027
ICD-10 code for dermatomyositis
Choose a code from the options below based on the documentation.
From the official ICD-10-CM alphabetic index entry “Dermatomyositis (acute) (chronic)”. Page updated September 29, 2026.
About coding dermatomyositis
The official ICD-10-CM index doesn't give a single default code for dermatomyositis; the code depends on the details below.
More specific dermatomyositis codes (official index)
- adult M33.10 — Other dermatomyositis, organ involvement unspecified
- in (due to) neoplastic disease D49.9 — Neoplasm of unspecified behavior of unspecified site
- juvenile M33.00 — Juvenile dermatomyositis, organ involvement unspecified
- with
- myopathy M33.02 — Juvenile dermatomyositis with myopathy
- respiratory involvement M33.01 — Juvenile dermatomyositis with respiratory involvement
- specified organ involvement NEC M33.09 — Juvenile dermatomyositis with other organ involvement
- amyopathic M33.03 — Juvenile dermatomyositis without myopathy
- without myopathy M33.03 — Juvenile dermatomyositis without myopathy
- specified NEC M33.10 — Other dermatomyositis, organ involvement unspecified
- with
- myopathy M33.12 — Other dermatomyositis with myopathy
- respiratory involvement M33.11 — Other dermatomyositis with respiratory involvement
- specified organ involvement NEC M33.19 — Other dermatomyositis with other organ involvement
- amyopathic M33.13 — Other dermatomyositis without myopathy
- without myopathy M33.13 — Other dermatomyositis without myopathy