ICD-10 code for Dighton's syndrome

The ICD-10-CM code for Dighton's syndrome is Q78.0 (Osteogenesis imperfecta).

Within Q78 (other osteochondrodysplasias), Q78.0 is specifically for Osteogenesis imperfecta. Related codes cover Polyostotic fibrous dysplasia (Q78.1), Osteopetrosis (Q78.2), progressive diaphyseal dysplasia (Q78.3), Enchondromatosis (Q78.4), Metaphyseal dysplasia (Q78.5), multiple congenital exostoses (Q78.6), other specified osteochondrodysplasias (Q78.8) and osteochondrodysplasia, unspecified (Q78.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 456 (Spinal Fusion Except Cervical with Spinal Curvature, Malignancy, or Infection with MCC, relative weight 7.6244), DRG 457 (Spinal Fusion Except Cervical with Spinal Curvature, Malignancy, or Infection with CC, relative weight 5.3668), DRG 458 (Spinal Fusion Except Cervical with Spinal Curvature, Malignancy, or Infection without CC/MCC, relative weight 4.0388), DRG 564 (Other Musculoskeletal System and Connective Tissue Diagnoses with MCC, relative weight 1.4908), DRG 565 (Other Musculoskeletal System and Connective Tissue Diagnoses with CC, relative weight 0.9783) and DRG 566 (Other Musculoskeletal System and Connective Tissue Diagnoses without CC/MCC, relative weight 0.7378), in MDC 08 (Diseases and Disorders of the Musculoskeletal System and Connective Tissue), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.