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ICD-10-CM 2027

ICD-10 code for disease krabbe's

E75.23

Krabbe disease

✓ Billable / specificCC — complication/comorbidity

From the official ICD-10-CM alphabetic index entry “Krabbe's › disease”. Page updated September 29, 2026.

About coding disease krabbe's

The ICD-10-CM code for disease krabbe's is E75.23 (Krabbe disease).

Within E75.2 (other sphingolipidosis), E75.23 is specifically for Krabbe disease. Related codes cover Fabry (-Anderson) disease (E75.21), Gaucher disease (E75.22), Niemann-Pick disease (E75.24), Metachromatic leukodystrophy (E75.25), Sulfatase deficiency (E75.26), Pelizaeus-Merzbacher disease (E75.27), Canavan disease (E75.28) and other sphingolipidosis (E75.29).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 056 (Degenerative Nervous System Disorders with MCC, relative weight 2.2655) and DRG 057 (Degenerative Nervous System Disorders without MCC, relative weight 1.2838), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

Common questions about disease krabbe's ICD-10 codes

What is the ICD-10 code for disease krabbe's?

E75.23 — Krabbe disease.

Is E75.23 billable?

Yes. E75.23 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can E75.23 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict E75.23 as a principal diagnosis.

Is E75.23 a CC or MCC?

E75.23 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.