ICD-10-CM 2027
ICD-10 code for Double aortic arch persistence
From the official ICD-10-CM alphabetic index entry “Persistence, persistent (congenital) › double aortic arch”. Page updated September 29, 2026.
About coding Double aortic arch persistence
The ICD-10-CM code for Double aortic arch persistence is Q25.45 (Double aortic arch).
Within Q25.4 (other congenital malformations of aorta), Q25.45 is specifically for Double aortic arch. Related codes cover congenital malformation of aorta unspecified (Q25.40), absence and aplasia of aorta (Q25.41), hypoplasia of aorta (Q25.42), congenital aneurysm of aorta (Q25.43), congenital dilation of aorta (Q25.44), Tortuous aortic arch (Q25.46), right aortic arch (Q25.47), anomalous origin of subclavian artery (Q25.48) and 1 more.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Double aortic arch persistence ICD-10 codes
What is the ICD-10 code for Double aortic arch persistence?
- Q25.45 — Double aortic arch.
Is Q25.45 billable?
- Yes. Q25.45 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q25.45 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q25.45 as a principal diagnosis.
Is Q25.45 a CC or MCC?
- Q25.45 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.