ICD-10-CM 2027
ICD-10 code for Ebstein's anomaly
From the official ICD-10-CM alphabetic index entry “Anomaly, anomalous (congenital) (unspecified type) › Ebstein's (heart) (tricuspid valve)”. Page updated September 29, 2026.
About coding Ebstein's anomaly
The ICD-10-CM code for Ebstein's anomaly is Q22.5 (Ebstein's anomaly).
Within Q22 (congenital malformations of pulmonary and tricuspid valves), Q22.5 is specifically for Ebstein's anomaly. Related codes cover pulmonary valve atresia (Q22.0), congenital pulmonary valve stenosis (Q22.1), congenital pulmonary valve insufficiency (Q22.2), other congenital malformations of pulmonary valve (Q22.3), congenital tricuspid stenosis (Q22.4), Hypoplastic right heart syndrome (Q22.6), other congenital malformations of tricuspid valve (Q22.8) and congenital malformation of tricuspid valve, unspecified (Q22.9).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about Ebstein's anomaly ICD-10 codes
What is the ICD-10 code for Ebstein's anomaly?
- Q22.5 — Ebstein's anomaly.
Is Q22.5 billable?
- Yes. Q22.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q22.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q22.5 as a principal diagnosis.
Is Q22.5 a CC or MCC?
- Q22.5 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.