Q22.1Congenital pulmonary valve stenosis

Q22.1 is the ICD-10-CM diagnosis code for congenital pulmonary valve stenosis. It belongs to category Q22 (congenital malformations of pulmonary and tricuspid valves), block Q20-Q28 (congenital malformations of the circulatory system) and chapter 17 (congenital malformations, deformations, chromosomal abnormalities, and genetic disorders). It is billable, so it can be reported on its own for dates of service from October 1, 2026 through September 30, 2027.

Within Q22 (congenital malformations of pulmonary and tricuspid valves), Q22.1 is specifically for congenital pulmonary valve stenosis. Related codes cover pulmonary valve atresia (Q22.0), congenital pulmonary valve insufficiency (Q22.2), other congenital malformations of pulmonary valve (Q22.3), congenital tricuspid stenosis (Q22.4), Ebstein's anomaly (Q22.5), Hypoplastic right heart syndrome (Q22.6), other congenital malformations of tricuspid valve (Q22.8) and congenital malformation of tricuspid valve, unspecified (Q22.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

It is exempt from present-on-admission (POA) reporting, so no POA indicator is required.

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Before ICD-10, this condition was coded in ICD-9-CM as 746.02 (stenosis of pulmonary valve, congenital).