ICD-10-CM 2027
ICD-10 code for ectodermal dysplasia
From the official ICD-10-CM alphabetic index entry “Dysplasia › ectodermal (anhidrotic) (congenital) (hereditary)”. Page updated September 29, 2026.
About coding ectodermal dysplasia
The ICD-10-CM code for ectodermal dysplasia is Q82.4 (Ectodermal dysplasia (anhidrotic)). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q82.4.
Within Q82 (other congenital malformations of skin), Q82.4 is specifically for ectodermal dysplasia (anhidrotic). Related codes cover hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6), other specified congenital malformations of skin (Q82.8) and congenital malformation of skin, unspecified (Q82.9).
Don't report Q82.4 together with the conditions in its Excludes1 note: Ellis-van Creveld syndrome (Q77.6).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
More specific ectodermal dysplasia codes (official index)
- hydrotic Q82.8 — Other specified congenital malformations of skin
Don't confuse with (Excludes1 for Q82.4)
- Ellis-van Creveld syndrome (Q77.6)
Common questions about ectodermal dysplasia ICD-10 codes
What is the ICD-10 code for ectodermal dysplasia?
- Q82.4 — Ectodermal dysplasia (anhidrotic). More specific codes apply when the documentation supports them: Q82.8.
What is the ICD-10 code for hydrotic ectodermal dysplasia?
- Q82.8 — Other specified congenital malformations of skin.
Is Q82.4 billable?
- Yes. Q82.4 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.4 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.4 as a principal diagnosis.
Is Q82.4 a CC or MCC?
- No. Q82.4 is neither a CC nor an MCC under MS-DRG v44.0.