ICD-10 code for endometrial stromal sarcoma

The ICD-10-CM code for endometrial stromal sarcoma is C54.1 (Malignant neoplasm of endometrium). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on C54.1.

Within C54 (malignant neoplasm of corpus uteri), C54.1 is specifically for malignant neoplasm of endometrium. Related codes cover isthmus uteri (C54.0), myometrium (C54.2), fundus uteri (C54.3), overlapping sites of corpus uteri (C54.8) and unspecified (C54.9).

It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.

In MS-DRG v44.0, it is part of the grouping logic for DRG 731 (Uterine and Adnexa Procedures for Malignancy with MCC, relative weight 3.5478), DRG 732 (Uterine and Adnexa Procedures for Malignancy with CC, relative weight 1.9208), DRG 733 (Uterine and Adnexa Procedures for Malignancy without CC/MCC, relative weight 1.4324), DRG 754 (Malignancy, Female Reproductive System with MCC, relative weight 1.8092), DRG 755 (Malignancy, Female Reproductive System with CC, relative weight 1.149) and DRG 756 (Malignancy, Female Reproductive System without CC/MCC, relative weight 0.8645), in MDC 13 (Diseases and Disorders of the Female Reproductive System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.