ICD-10-CM 2027
ICD-10 code for fish odor syndrome
Other specified disorders of amino-acid metabolism
From the official ICD-10-CM alphabetic index entry “Syndrome › fish odor”. Page updated September 29, 2026.
About coding fish odor syndrome
The ICD-10-CM code for fish odor syndrome is E72.89 (Other specified disorders of amino-acid metabolism).
Within E72.8, choose E72.89 (Other specified disorders of amino-acid metabolism) only when documentation doesn't support a more specific option: disorders of gamma aminobutyric acid metabolism (E72.81).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about fish odor syndrome ICD-10 codes
What is the ICD-10 code for fish odor syndrome?
- E72.89 — Other specified disorders of amino-acid metabolism.
Is E72.89 billable?
- Yes. E72.89 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E72.89 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E72.89 as a principal diagnosis.
Is E72.89 a CC or MCC?
- E72.89 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.