ICD-10-CM 2027
ICD-10 code for gamma sarcoglycanopathy
From the official ICD-10-CM alphabetic index entry “Sarcoglycanopathy › gamma”. Page updated September 29, 2026.
About coding gamma sarcoglycanopathy
The ICD-10-CM code for gamma sarcoglycanopathy is G71.0349 (Limb girdle muscular dystrophy due to other sarcoglycan dysfunction).
Within G71.034, choose G71.0349 (other sarcoglycan dysfunction) only when documentation doesn't support a more specific option: unspecified (G71.0340), alpha sarcoglycan dysfunction (G71.0341) and beta sarcoglycan dysfunction (G71.0342).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 091 (Other Disorders of Nervous System with MCC, relative weight 1.7046), DRG 092 (Other Disorders of Nervous System with CC, relative weight 1.0239) and DRG 093 (Other Disorders of Nervous System without CC/MCC, relative weight 0.7783), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about gamma sarcoglycanopathy ICD-10 codes
What is the ICD-10 code for gamma sarcoglycanopathy?
- G71.0349 — Limb girdle muscular dystrophy due to other sarcoglycan dysfunction.
Is G71.0349 billable?
- Yes. G71.0349 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can G71.0349 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict G71.0349 as a principal diagnosis.
Is G71.0349 a CC or MCC?
- No. G71.0349 is neither a CC nor an MCC under MS-DRG v44.0.