ICD-10-CM 2027
ICD-10 code for Gerstmann-Sträussler-Scheinker syndrome
From the official ICD-10-CM alphabetic index entry “Gerstmann-Sträussler-Scheinker syndrome (GSS)”. Page updated October 2, 2026.
About coding Gerstmann-Sträussler-Scheinker syndrome
The ICD-10-CM code for Gerstmann-Sträussler-Scheinker syndrome is A81.82 (Gerstmann-Straussler-Scheinker syndrome).
Within A81.8 (other atypical virus infections of central nervous system), A81.82 is specifically for Gerstmann-Straussler-Scheinker syndrome. Related codes cover Kuru (A81.81), Fatal familial insomnia (A81.83) and other atypical virus infections of central nervous system (A81.89).
Use an additional code, if applicable, to identify: dementia with anxiety (F02.84, F02.A4, F02.B4, F02.C4), dementia with behavioral disturbance (F02.81-, F02.A1-, F02.B1-, F02.C1-), dementia with mood disturbance (F02.83, F02.A3, F02.B3, F02.C3), dementia with psychotic disturbance (F02.82, F02.A2, F02.B2, F02.C2), dementia without behavioral disturbance (F02.80, F02.A0, F02.B0, F02.C0) and 1 more.
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
Common questions about Gerstmann-Sträussler-Scheinker syndrome ICD-10 codes
What is the ICD-10 code for Gerstmann-Sträussler-Scheinker syndrome?
- A81.82 — Gerstmann-Straussler-Scheinker syndrome.
Is A81.82 billable?
- Yes. A81.82 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can A81.82 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict A81.82 as a principal diagnosis.
Is A81.82 a CC or MCC?
- A81.82 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.