ICD-10-CM 2027
ICD-10 code for hemophilia
From the official ICD-10-CM alphabetic index entry “Hemophilia (classical) (familial) (hereditary)”. Page updated September 29, 2026.
About coding hemophilia
The ICD-10-CM code for hemophilia is D66 (Hereditary factor VIII deficiency). The official index lists 8 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on D66.
Don't report D66 together with the conditions in its Excludes1 note: factor VIII deficiency with vascular defect (D68.0-).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 813 (Coagulation Disorders, relative weight 1.5257), in MDC 16 (Diseases and Disorders of the Blood and Blood Forming Organs and Immunological Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific hemophilia codes (official index)
- A D66 — Hereditary factor VIII deficiency
- B D67 — Hereditary factor IX deficiency
- C D68.1 — Hereditary factor XI deficiency
- acquired D68.311 — Acquired hemophilia
- autoimmune D68.311 — Acquired hemophilia
- calcipriva D68.4 — Acquired coagulation factor deficiency
- nonfamilial D68.4 — Acquired coagulation factor deficiency
- secondary D68.311 — Acquired hemophilia
- vascular
Don't confuse with (Excludes1 for D66)
- factor VIII deficiency with vascular defect (D68.0-)
Common questions about hemophilia ICD-10 codes
What is the ICD-10 code for hemophilia?
- D66 — Hereditary factor VIII deficiency. More specific codes apply when the documentation supports them: D66, D67, D68.1, D68.311 and others below.
What is the ICD-10 code for a hemophilia?
- D66 — Hereditary factor VIII deficiency.
What is the ICD-10 code for b hemophilia?
- D67 — Hereditary factor IX deficiency.
What is the ICD-10 code for c hemophilia?
- D68.1 — Hereditary factor XI deficiency.
What is the ICD-10 code for acquired hemophilia?
- D68.311 — Acquired hemophilia.
What is the ICD-10 code for autoimmune hemophilia?
- D68.311 — Acquired hemophilia.
What is the ICD-10 code for calcipriva hemophilia?
- D68.4 — Acquired coagulation factor deficiency.
Is D66 billable?
- Yes. D66 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can D66 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict D66 as a principal diagnosis.
Is D66 a CC or MCC?
- D66 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.