D68.0Von Willebrand disease

D68.0 is the ICD-10-CM diagnosis code for von Willebrand disease. It belongs to category D68 (other coagulation defects), block D65-D69 (coagulation defects, purpura and other hemorrhagic conditions) and chapter 3 (diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism). It is a header code, so it can't be reported by itself; one of its 6 subcodes must be used instead.

Within D68 (other coagulation defects), D68.0 is specifically for von Willebrand disease. Related codes cover hereditary factor XI deficiency (D68.1), hereditary deficiency of other clotting factors (D68.2), hemorrhagic disorder due to circulating anticoagulants (D68.3), acquired coagulation factor deficiency (D68.4), primary thrombophilia (D68.5), other thrombophilia (D68.6), other specified coagulation defects (D68.8) and coagulation defect, unspecified (D68.9).

To report this condition, pick the subcode that matches the documentation: D68.00 (unspecified), D68.01 (type 1), D68.02 (type 2), D68.03 (type 3), D68.04 (disease) and D68.09 (disease).

Don't report D68.0 together with the conditions in its Excludes1 note: capillary fragility (hereditary) (D69.8), factor VIII deficiency NOS (D66) and factor VIII deficiency with functional defect (D66).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015, and changed in FY2023 (title revised).

Before ICD-10, this condition was coded in ICD-9-CM as 286.4 (von Willebrand's disease).