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ICD-10-CM 2027

ICD-10 code for Kearns-Sayre syndrome

H49.81

Kearns-Sayre syndrome

Header — needs a more specific code

From the official ICD-10-CM alphabetic index entry “Kearns-Sayre syndrome”. Page updated September 29, 2026.

About coding Kearns-Sayre syndrome

The ICD-10-CM code for Kearns-Sayre syndrome is H49.81 (Kearns-Sayre syndrome).

Within H49.8 (other paralytic strabismus), H49.81 is specifically for Kearns-Sayre syndrome. Related codes cover other paralytic strabismus (H49.88).

To report this condition, pick the subcode that matches the documentation: H49.811 (right eye), H49.812 (left eye), H49.813 (bilateral) and H49.819 (unspecified eye).

It has been part of ICD-10-CM since the code set took effect on October 1, 2015 and hasn't changed since.

Common questions about Kearns-Sayre syndrome ICD-10 codes

What is the ICD-10 code for Kearns-Sayre syndrome?

H49.81 — Kearns-Sayre syndrome (a header code; report a more specific subcode).

Is H49.81 billable?

No. H49.81 is a header code. Report one of its more specific subcodes instead.