ICD-10-CM 2027
ICD-10 code for ketone metabolism disorder
From the official ICD-10-CM alphabetic index entry “Disorder (of) › ketone metabolism”. Page updated September 29, 2026.
About coding ketone metabolism disorder
The ICD-10-CM code for ketone metabolism disorder is E71.32 (Disorders of ketone metabolism).
Within E71.3 (disorders of fatty-acid metabolism), E71.32 is specifically for disorders of ketone metabolism. Related codes cover disorder of fatty-acid metabolism, unspecified (E71.30), disorders of fatty-acid oxidation (E71.31) and other disorders of fatty-acid metabolism (E71.39).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about ketone metabolism disorder ICD-10 codes
What is the ICD-10 code for ketone metabolism disorder?
- E71.32 — Disorders of ketone metabolism.
Is E71.32 billable?
- Yes. E71.32 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.32 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.32 as a principal diagnosis.
Is E71.32 a CC or MCC?
- E71.32 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.