ICD-10-CM 2027
ICD-10 code for LCAD deficiency
Long chain/very long chain acyl CoA dehydrogenase deficiency
From the official ICD-10-CM alphabetic index entry “Deficiency, deficient › LCAD (long chain acyl CoA dehydrogenase deficiency)”. Page updated September 29, 2026.
About coding LCAD deficiency
The ICD-10-CM code for LCAD deficiency is E71.310 (Long chain/very long chain acyl CoA dehydrogenase deficiency).
Within E71.31 (disorders of fatty-acid oxidation), E71.310 is specifically for long chain/very long chain acyl CoA dehydrogenase deficiency. Related codes cover Medium chain acyl CoA dehydrogenase deficiency (E71.311), short chain acyl CoA dehydrogenase deficiency (E71.312), Glutaric aciduria type II (E71.313), muscle carnitine palmitoyltransferase deficiency (E71.314) and other disorders of fatty-acid oxidation (E71.318).
As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 642 (Inborn and Other Disorders of Metabolism, relative weight 1.3219), in MDC 10 (Endocrine, Nutritional and Metabolic Diseases and Disorders), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about LCAD deficiency ICD-10 codes
What is the ICD-10 code for LCAD deficiency?
- E71.310 — Long chain/very long chain acyl CoA dehydrogenase deficiency.
Is E71.310 billable?
- Yes. E71.310 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can E71.310 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict E71.310 as a principal diagnosis.
Is E71.310 a CC or MCC?
- E71.310 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.