ICD-10-CM 2027
ICD-10 code for lung absence
From the official ICD-10-CM alphabetic index entry “Absence (of) (organ or part) (complete or partial) › lung (fissure) (lobe) (bilateral) (unilateral) (congenital)”. Page updated September 29, 2026.
About coding lung absence
The ICD-10-CM code for lung absence is Q33.3 (Agenesis of lung). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q33.3.
Within Q33 (congenital malformations of lung), Q33.3 is specifically for agenesis of lung. Related codes cover congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
In MS-DRG v44.0, it is part of the grouping logic for DRG 205 (Other Respiratory System Diagnoses with MCC, relative weight 1.8244) and DRG 206 (Other Respiratory System Diagnoses without MCC, relative weight 0.9257), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
More specific lung absence codes (official index)
- acquired (any part) Z90.2 — Acquired absence of lung [part of]
Common questions about lung absence ICD-10 codes
What is the ICD-10 code for lung absence?
- Q33.3 — Agenesis of lung. More specific codes apply when the documentation supports them: Z90.2.
What is the ICD-10 code for acquired lung absence?
- Z90.2 — Acquired absence of lung [part of].
Is Q33.3 billable?
- Yes. Q33.3 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q33.3 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q33.3 as a principal diagnosis.
Is Q33.3 a CC or MCC?
- Q33.3 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.