ICD-10 code for lung agenesis

The ICD-10-CM code for lung agenesis is Q33.3 (Agenesis of lung).

Within Q33 (congenital malformations of lung), Q33.3 is specifically for agenesis of lung. Related codes cover congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), congenital hypoplasia and dysplasia of lung (Q33.6), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 205 (Other Respiratory System Diagnoses with MCC, relative weight 1.8244) and DRG 206 (Other Respiratory System Diagnoses without MCC, relative weight 0.9257), in MDC 04 (Diseases and Disorders of the Respiratory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.