ICD-10 code for Lymphoplasmacytic lymphoma

The ICD-10-CM code for Lymphoplasmacytic lymphoma is C83.0 (Small cell B-cell lymphoma). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on C83.0.

Within C83 (non-follicular lymphoma), C83.0 is specifically for small cell B-cell lymphoma. Related codes cover Mantle cell lymphoma (C83.1), diffuse large B-cell lymphoma (C83.3), lymphoblastic (diffuse) lymphoma (C83.5), Burkitt lymphoma (C83.7), other non-follicular lymphoma (C83.8) and non-follicular (diffuse) lymphoma, unspecified (C83.9).

To report this condition, pick the subcode that matches the documentation: C83.00 (unspecified site), C83.01 (lymph nodes of head, face, and neck), C83.02 (intrathoracic lymph nodes), C83.03 (intra-abdominal lymph nodes), C83.04 (lymph nodes of axilla and upper limb), C83.05 (lymph nodes of inguinal region and lower limb), C83.06 (intrapelvic lymph nodes), C83.07 (spleen) and 3 more.

Don't report C83.0 together with the conditions in its Excludes1 note: chronic lymphocytic leukemia (C91.1), mature T/NK-cell lymphomas (C84.-) and Waldenström macroglobulinemia (C88.00).