ICD-10 code for malignant paraganglioma

The ICD-10-CM code for malignant paraganglioma is C75.5 (Malignant neoplasm of aortic body and other paraganglia). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on C75.5.

Within C75, choose C75.5 (of aortic body and other paraganglia) only when documentation doesn't support a more specific option: of parathyroid gland (C75.0), of pituitary gland (C75.1), of craniopharyngeal duct (C75.2), of pineal gland (C75.3), of carotid body (C75.4), with pluriglandular involvement, unspecified (C75.8) and of endocrine gland, unspecified (C75.9).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 054 (Nervous System Neoplasms with MCC, relative weight 1.5194) and DRG 055 (Nervous System Neoplasms without MCC, relative weight 1.0296), in MDC 01 (Diseases and Disorders of the Nervous System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.