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ICD-10-CM 2027

ICD-10 code for marginal zone lymphoma (MALT)

C88.40

Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission

✓ Billable / specificCC — complication/comorbidity

Confirmed by the official ICD-10-CM index entry “lymphoma (of) (malignant) › extranodal marginal zone b-cell lymphoma of mucosa-associated lymphoid tissue [malt-lymphoma]”. Page updated September 29, 2026.

About coding marginal zone lymphoma (MALT)

The ICD-10-CM code for marginal zone lymphoma (MALT) is C88.40 (Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission). The official index lists 12 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on C88.40.

It is also searched as MALT lymphoma.

Within C88.4 (extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma]), C88.40 is specifically for extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission. Related codes cover in remission (C88.41).

As a secondary diagnosis it is a CC (complication or comorbidity), which can move an inpatient stay into the "with CC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 820 (Lymphoma and Leukemia with Major O.R. Procedures with MCC, relative weight 6.2481), DRG 821 (Lymphoma and Leukemia with Major O.R. Procedures with CC, relative weight 2.2023), DRG 822 (Lymphoma and Leukemia with Major O.R. Procedures without CC/MCC, relative weight 1.1272), DRG 823 (Lymphoma and Non-Acute Leukemia with Other Procedures with MCC, relative weight 4.6059), DRG 824 (Lymphoma and Non-Acute Leukemia with Other Procedures with CC, relative weight 2.2515), DRG 825 (Lymphoma and Non-Acute Leukemia with Other Procedures without CC/MCC, relative weight 1.2995) and 6 more, in MDC 17 (Myeloproliferative Diseases and Disorders, Poorly Differentiated Neoplasms) and MDC 25 (Human Immunodeficiency Virus Infections), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.

Related Marginal zone lymphoma (MALT) codes

  • C83.00 Small cell B-cell lymphoma, unspecified site
  • C83.01 Small cell B-cell lymphoma, lymph nodes of head, face, and neck
  • C83.02 Small cell B-cell lymphoma, intrathoracic lymph nodes
  • C83.03 Small cell B-cell lymphoma, intra-abdominal lymph nodes
  • C83.04 Small cell B-cell lymphoma, lymph nodes of axilla and upper limb
  • C83.05 Small cell B-cell lymphoma, lymph nodes of inguinal region and lower limb
  • C83.06 Small cell B-cell lymphoma, intrapelvic lymph nodes
  • C83.07 Small cell B-cell lymphoma, spleen
  • C83.08 Small cell B-cell lymphoma, lymph nodes of multiple sites
  • C83.09 Small cell B-cell lymphoma, extranodal and solid organ sites
  • C83.0A Small cell B-cell lymphoma, in remission
  • C88.41 Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma], in remission

Common questions about marginal zone lymphoma (MALT) ICD-10 codes

What is the ICD-10 code for marginal zone lymphoma (MALT)?

C88.40 — Extranodal marginal zone B-cell lymphoma of mucosa-associated lymphoid tissue [MALT-lymphoma] not having achieved remission. More specific codes apply when the documentation supports them: C83.00, C83.01, C83.02, C83.03 and others below.

What is the ICD-10 code for small cell b-cell lymphoma, unspecified site?

C83.00 — Small cell B-cell lymphoma, unspecified site.

What is the ICD-10 code for small cell b-cell lymphoma, lymph nodes of head, face, and neck?

C83.01 — Small cell B-cell lymphoma, lymph nodes of head, face, and neck.

What is the ICD-10 code for small cell b-cell lymphoma, intrathoracic lymph nodes?

C83.02 — Small cell B-cell lymphoma, intrathoracic lymph nodes.

What is the ICD-10 code for small cell b-cell lymphoma, intra-abdominal lymph nodes?

C83.03 — Small cell B-cell lymphoma, intra-abdominal lymph nodes.

What is the ICD-10 code for small cell b-cell lymphoma, lymph nodes of axilla and upper limb?

C83.04 — Small cell B-cell lymphoma, lymph nodes of axilla and upper limb.

What is the ICD-10 code for small cell b-cell lymphoma, lymph nodes of inguinal region and lower limb?

C83.05 — Small cell B-cell lymphoma, lymph nodes of inguinal region and lower limb.

Is C88.40 billable?

Yes. C88.40 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).

Can C88.40 be used as a principal diagnosis?

Yes. The Medicare Code Editor doesn't restrict C88.40 as a principal diagnosis.

Is C88.40 a CC or MCC?

C88.40 is a CC (complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.