ICD-10-CM 2027
ICD-10 code for pigmentosum xeroderma
From the official ICD-10-CM alphabetic index entry “Xeroderma › pigmentosum”. Page updated September 29, 2026.
About coding pigmentosum xeroderma
The ICD-10-CM code for pigmentosum xeroderma is Q82.1 (Xeroderma pigmentosum).
Within Q82 (other congenital malformations of skin), Q82.1 is specifically for Xeroderma pigmentosum. Related codes cover hereditary lymphedema (Q82.0), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital non-neoplastic nevus (Q82.5), congenital sacral dimple (Q82.6), other specified congenital malformations of skin (Q82.8) and congenital malformation of skin, unspecified (Q82.9).
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
In MS-DRG v44.0, it is part of the grouping logic for DRG 606 (Minor Skin Disorders with MCC, relative weight 1.5728), DRG 607 (Minor Skin Disorders without MCC, relative weight 0.8772) and DRG 795 (Normal Newborn, relative weight 0.2022), in MDC 09 (Diseases and Disorders of the Skin, Subcutaneous Tissue and Breast) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.
Common questions about pigmentosum xeroderma ICD-10 codes
What is the ICD-10 code for pigmentosum xeroderma?
- Q82.1 — Xeroderma pigmentosum.
Is Q82.1 billable?
- Yes. Q82.1 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.1 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.1 as a principal diagnosis.
Is Q82.1 a CC or MCC?
- No. Q82.1 is neither a CC nor an MCC under MS-DRG v44.0.