ICD-10-CM 2027
ICD-10 code for Port wine mark
From the official ICD-10-CM alphabetic index entry “Mark › port wine”. Page updated September 29, 2026.
About coding Port wine mark
The ICD-10-CM code for Port wine mark is Q82.5 (Congenital non-neoplastic nevus).
Within Q82 (other congenital malformations of skin), Q82.5 is specifically for congenital non-neoplastic nevus. Related codes cover hereditary lymphedema (Q82.0), Xeroderma pigmentosum (Q82.1), congenital cutaneous mastocytosis (Q82.2), Incontinentia pigmenti (Q82.3), ectodermal dysplasia (anhidrotic) (Q82.4), congenital sacral dimple (Q82.6), other specified congenital malformations of skin (Q82.8) and congenital malformation of skin, unspecified (Q82.9).
The conditions in its Excludes2 note aren't part of Q82.5, but may be coded alongside it if the patient has both: Café au lait spots (L81.3), lentigo (L81.4), nevus NOS (D22.-), araneus nevus (I78.1) and 4 more.
It is not a CC or MCC, so as a secondary diagnosis it doesn't change the MS-DRG severity level.
Common questions about Port wine mark ICD-10 codes
What is the ICD-10 code for Port wine mark?
- Q82.5 — Congenital non-neoplastic nevus.
Is Q82.5 billable?
- Yes. Q82.5 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q82.5 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q82.5 as a principal diagnosis.
Is Q82.5 a CC or MCC?
- No. Q82.5 is neither a CC nor an MCC under MS-DRG v44.0.