ICD-10 code for pulmonary artery atresia

The ICD-10-CM code for pulmonary artery atresia is Q25.5 (Atresia of pulmonary artery). The official index lists 1 more specific code, so check the documentation for details such as type, cause, site or severity before settling on Q25.5.

Within Q25 (congenital malformations of great arteries), Q25.5 is specifically for atresia of pulmonary artery. Related codes cover Patent ductus arteriosus (Q25.0), coarctation of aorta (Q25.1), atresia of aorta (Q25.2), Supravalvular aortic stenosis (Q25.3), other congenital malformations of aorta (Q25.4), stenosis of pulmonary artery (Q25.6), other congenital malformations of pulmonary artery (Q25.7), other congenital malformations of other great arteries (Q25.8) and 1 more.

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 306 (Cardiac Congenital and Valvular Disorders with MCC, relative weight 1.546) and DRG 307 (Cardiac Congenital and Valvular Disorders without MCC, relative weight 0.9148), in MDC 05 (Diseases and Disorders of the Circulatory System), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.