ICD-10-CM 2027
ICD-10 code for pulmonary hypoplasia
Congenital hypoplasia and dysplasia of lung
From the official ICD-10-CM alphabetic index entry “Hypoplasia, hypoplastic › pulmonary (not associated with short gestation)”. Page updated September 29, 2026.
About coding pulmonary hypoplasia
The ICD-10-CM code for pulmonary hypoplasia is Q33.6 (Congenital hypoplasia and dysplasia of lung). The official index lists 2 more specific codes, so check the documentation for details such as type, cause, site or severity before settling on Q33.6.
Within Q33 (congenital malformations of lung), Q33.6 is specifically for congenital hypoplasia and dysplasia of lung. Related codes cover congenital cystic lung (Q33.0), accessory lobe of lung (Q33.1), sequestration of lung (Q33.2), agenesis of lung (Q33.3), congenital bronchiectasis (Q33.4), ectopic tissue in lung (Q33.5), other congenital malformations of lung (Q33.8) and congenital malformation of lung, unspecified (Q33.9).
Don't report Q33.6 together with the conditions in its Excludes1 note: pulmonary hypoplasia associated with short gestation (P28.0).
As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.
More specific pulmonary hypoplasia codes (official index)
Don't confuse with (Excludes1 for Q33.6)
- pulmonary hypoplasia associated with short gestation (P28.0)
Common questions about pulmonary hypoplasia ICD-10 codes
What is the ICD-10 code for pulmonary hypoplasia?
- Q33.6 — Congenital hypoplasia and dysplasia of lung. More specific codes apply when the documentation supports them: J43.0, P28.0.
What is the ICD-10 code for associated with short gestation pulmonary hypoplasia?
- P28.0 — Primary atelectasis of newborn.
Is Q33.6 billable?
- Yes. Q33.6 is a billable/specific ICD-10-CM code valid for FY2027 (October 1, 2026 – September 30, 2027).
Can Q33.6 be used as a principal diagnosis?
- Yes. The Medicare Code Editor doesn't restrict Q33.6 as a principal diagnosis.
Is Q33.6 a CC or MCC?
- Q33.6 is an MCC (major complication or comorbidity) under MS-DRG v44.0, unless excluded by the principal diagnosis.