ICD-10 code for pulmonary interstitial glycogenosis

The ICD-10-CM code for pulmonary interstitial glycogenosis is J84.842 (Pulmonary interstitial glycogenosis).

Within J84.84 (other interstitial lung diseases of childhood), J84.842 is specifically for pulmonary interstitial glycogenosis. Related codes cover neuroendocrine cell hyperplasia of infancy (J84.841), alveolar capillary dysplasia with vein misalignment (J84.843) and other interstitial lung diseases of childhood (J84.848).

As a secondary diagnosis it is an MCC (major complication or comorbidity), which can move an inpatient stay into the highest-paying "with MCC" MS-DRG of its family, unless the principal diagnosis excludes it.

In MS-DRG v44.0, it is part of the grouping logic for DRG 196 (Interstitial Lung Disease with MCC, relative weight 1.8336), DRG 197 (Interstitial Lung Disease with CC, relative weight 0.9492), DRG 198 (Interstitial Lung Disease without CC/MCC, relative weight 0.7259), DRG 791 (Prematurity with Major Problems, relative weight 4.1075) and DRG 793 (Full Term Neonate with Major Problems, relative weight 4.2195), in MDC 04 (Diseases and Disorders of the Respiratory System) and MDC 15 (Newborns and Other Neonates with Conditions Originating in the Perinatal Period), as a principal or secondary diagnosis. The DRG a claim lands in depends on the principal diagnosis, procedures and any CC/MCC secondary diagnoses.